Tehran University of Medical Sciences Frontiers in Dentistry 2676-296X 13 2 2016 10 10 133 138 EN Najmeh Akhlaghi Dental Research Center, Department of Pediatric Dentistry, School of Dentistry, Isfahan University of Medical Sciences, Isfahan, Iran. Ali-Reza Eshghi Dental Research Center, Department of Pediatric Dentistry, School of Dentistry, Isfahan University of Medical Sciences, Isfahan, Iran. Mehrnaz Mohamadpour Dental Research Center, Department of Pediatric Dentistry, School of Dentistry, Isfahan University of Medical Sciences, Isfahan, Iran. 2016 05 22 2016 05 25 Dentinogenesis imperfecta (DI) is a hereditary dentin defect caused by an autosomal dominant mutation in dentin sialophosphoprotein gene. Defective dentin development results in discolored teeth that are prone to wear and fracture. Early diagnosis and proper treatment are necessary to achieve better functional and esthetic results and minimize nutritional deficiencies and psychosocial distress. In order to prevent excessive loss of tooth structure, placement of stainless steel crowns (SSCs) on deciduous and young permanent posterior teeth is recommended as soon as such teeth erupt. This clinical report presents the clinical manifestations and management of a 3.5-year-old child diagnosed with DI type II. Keywords: Dentin; Dentinogenesis Imperfecta; Tooth, Deciduous https://fid.tums.ac.ir/index.php/fid/article/view/1251 https://fid.tums.ac.ir/index.php/fid/article/download/1251/879