Oral Rehabilitation of a Patient with Papillon Lefèvre Syndrome Using Fixed Full-Arch Hybrid Prostheses Supported by Four Axially Loaded Implants: A Case Report with Four-Year Follow-up
Dental Implants in a Papillon Lefèvre Patient
-
Kumar Sharma Pawan
,
Vasudevan Karthikeyan
,
Krishnan Murugesan
,
Balasubramaniam Muthukumar
,
Krishna Kumar Raja
,
Sivanesan Karthikeyan Jagdish
Abstract
This report details the successful prosthetic rehabilitation of a 25-year-old male patient with Papillon Lefèvre Syndrome (PLS) using an implant-supported hybrid prosthesis. Six implants were placed in the maxilla, and four were placed in the mandibular arch. All implants were inserted axially (non-tilted) and were planned to be loaded after a healing period of 6 months. One implant failed due to graft loss during the healing phase, which was removed and the remaining implants were restored with a hybrid prosthesis after 6 months, using the delayed loading protocol. The patient was followed-up for four years and all the remaining implants successfully integrated and remained fully functional during this period. The prosthesis significantly improved the functional, aesthetic, and psychological well-being of the patient. This case report is the first of its kind to use only four axially placed implants for rehabilitation of a PLS patient with a successful four-year follow-up.
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13. Peñarrocha-Oltra D, Peñarrocha-Diago M, Balaguer-Martínez J, Ata-Ali J, Peñarrocha-Diago M. Full-arch fixed prosthesis supported by four implants in patients with recessive dystrophic epidermolysis bullosa. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2011 Aug;112(2):e4-10.
14. Atarbashi-Moghadam F, Atarbashi-Moghadam S, Kazemifard S, Sijanivandi S, Namdari M. Oral rehabilitation of Papillon-Lefèvre syndrome patients by dental implants: a systematic review. J Korean Assoc Oral Maxillofac Surg. 2020 Aug 31;46(4):220-227.
2. Dhanrajani PJ. Papillon-Lefevre syndrome: clinical presentation and a brief review. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2009 Jul;108(1):e1-7.
3. Sreeramulu B, Haragopal S, Shalini K, Sudha MD, Kiran G. The prosthodontic management of a young edentulous patient with the papillon lefevre syndrome-a rare case report. J Clin Diagn Res. 2012 Dec;6(10):1808-11.
4. Tyagi S, Thomas AM, Balla V, Kundra R. Cu-sil dentures: A novel approach of Papillon-Lefèvre syndrome management. J Indian Soc Pedod Prev Dent. 2019 Jul-Sep;37(3):303-307.
5. Nassani MZ, Al-Maweri SA, Veeraganta SK, Al-Shamiri HM, Alaizari NA, Najeeb S. Survival Rates of Dental Implants in Patients with Papillon-Lefévre Syndrome: A Systematic Review. J Contemp Dent Pract. 2021 Jan 1;22(1):93-100.
6. Ahmadian L, Monzavi A, Arbabi R, Hashemi HM. Full-mouth rehabilitation of an edentulous patient with Papillon-Lefèvre syndrome using dental implants: a clinical report. J Prosthodont. 2011 Dec;20(8):643-8.
7. Kinaia BM, Hope K, Zuhaili A, Tulasne JF. Full-Mouth Rehabilitation with Calvarium Bone Grafts and Dental Implants for a Papillon-Lefèvre Syndrome Patient: Case Report. Int J Oral Maxillofac Implants. 2017 Nov/Dec;32(6):e259-e264.
8. Etöz OA, Ulu M, Kesim B. Treatment of patient with Papillon-Lefevre syndrome with short dental implants: a case report. Implant Dent. 2010 Oct;19(5):394-9.
9. Maló P, Rangert B, Nobre M. "All-on-Four" immediate-function concept with Brånemark System implants for completely edentulous mandibles: a retrospective clinical study. Clin Implant Dent Relat Res. 2003;5 Suppl 1:2-9.
10. Penarrocha M, Rambla J, Balaguer J, Serrano C, Silvestre J, Bagán JV. Complete fixed prostheses over implants in patients with oral epidermolysis bullosa. J Oral Maxillofac Surg. 2007 Jul;65(7 Suppl 1):103-6.
11. Lee H, Al Mardini M, Ercoli C, Smith MN. Oral rehabilitation of a completely edentulous epidermolysis bullosa patient with an implant-supported prosthesis: a clinical report. J Prosthet Dent. 2007 Feb;97(2):65-9.
12. Muller F, Bergendal B, Wahlmann U, Wagner W. Implant-supported fixed dental prostheses in an edentulous patient with dystrophic epidermolysis bullosa. Int J Prosthodont. 2010 Jan-Feb;23(1):42-8.
13. Peñarrocha-Oltra D, Peñarrocha-Diago M, Balaguer-Martínez J, Ata-Ali J, Peñarrocha-Diago M. Full-arch fixed prosthesis supported by four implants in patients with recessive dystrophic epidermolysis bullosa. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2011 Aug;112(2):e4-10.
14. Atarbashi-Moghadam F, Atarbashi-Moghadam S, Kazemifard S, Sijanivandi S, Namdari M. Oral rehabilitation of Papillon-Lefèvre syndrome patients by dental implants: a systematic review. J Korean Assoc Oral Maxillofac Surg. 2020 Aug 31;46(4):220-227.
| Issue | Vol 20 (Continuously Published Article-Based) | |
| Section | Case Report | |
| DOI | https://doi.org/10.18502/fid.v20i7.12606 | |
| Keywords | ||
| Dental Implants Dental Prosthesis Implant-Supported Mouth Rehabilitation Papillon-Lefevre Disease | ||
| Rights and permissions | |
|
This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License. |
How to Cite
1.
Pawan K, Karthikeyan V, Murugesan K, Muthukumar B, Raja K, Jagdish S. Oral Rehabilitation of a Patient with Papillon Lefèvre Syndrome Using Fixed Full-Arch Hybrid Prostheses Supported by Four Axially Loaded Implants: A Case Report with Four-Year Follow-up. Front Dent. 2023;20:1-6.
